Sickle cell anemia
Moyamoya syndrome is sometimes seen in association with other diseases and can be a relatively uncommon neurovascular complication of sickle cell anemia. Moyamoya syndrome is most commonly seen in children and young adults and is typically diagnosed in children 10 years of age and younger, as well as in adults (more commonly women) in their 30’s. Patients present with symptoms related to this vessel blockage resulting in stroke, transient neurologic deficit and seizure.
Moyamoya disease is a rare vascular disease of the brain, characterized by progressive blockage of the large branches of the internal carotid artery of the brain. To feed the starved cerebral tissue caused by Moyamoya disease, the body forms a network of dilated and weakened (friable) blood vessels. When viewed on a diagnostic cerebral angiography test, the blood vessels resemble a “puff of smoke.” This disease was originally identified in Japanese patients. Moyamoya is the Japanese word for the “puff of smoke” appearance.
The Moyamoya Center at Northwell Health Neuroscience Institute is a multidisciplinary group dedicated to the diagnosis, treatment and support of patients and families with Moyamoya disease and other neurosurgical and neurological conditions. Members of the team include a vascular neurologist, pediatric neurologist, neurosurgeon, endovascular specialists, neuroradiologists, neuroscience nurses and physicians assistants. Our center works closely with the neurological specialists at the Stroke Center and the Brain Aneurysm Center within the Northwell Health Neuroscience Institute
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The Moyamoya Center of Northwell Health Neuroscience Institute ensures the best neurological care for yourself and your family, including thorough neurological evaluations, the latest diagnostic technology and the most advanced treatment options.