Biliary cirrhosis is a rare form of liver cirrhosis caused by disease or defects of the bile ducts. Symptoms usually include cholestasis (accumulation of bile in the liver).
There are two types of biliary cirrhosis:
- Primary biliary cirrhosis - Inflammation and destruction of bile ducts in the liver, usually due to an autoimmune disease in which the body's immune system mistakenly attacks healthy tissues.
- Secondary biliary cirrhosis - This results from prolonged bile duct obstruction or narrowing or closure of the bile duct for other reasons, such as a tumor.