Choroid Plexus Papilloma

Choroid Plexus Papilloma

Choroid plexus papillomas are uncommon, benign neuroepithelial intraventricular tumors, which can occur in the adult population but are more common in children. Choroid plexus papillomas are classified as a grade I tumors if typical and if atypical as grade II tumors. They typically appear as cauliflower-like masses. Choroid plexus papillomas are far more common than the more aggressive choroid plexus carcinoma (grade III) by a ratio of 5:1.

With imaging, these tumors are usually identified in the fourth ventricle in adults and in the lateral ventricles in the pediatric population. Choroid plexus papillomas appear as solid vascular tumors with vivid frond-like pattern enhancement. In 25% of all cases, speckled calcifications are present.

About 85% of all choroid plexus papillomas occur in children under 5 years of age. Choroid plexus papillomas account for approximately 1% of all brain tumors, 2-6% of all pediatric brain tumors and 0.5% of adult brain tumors.

Significant hydrocephalus is very common and is witnessed in over 80% of all cases. The exact tumor mechanism remains uncertain, but it is believed to be a combination of cerebrospinal fluid overproduction and decreased arachnoid granulation reabsorption.

Choroid Plexus Carcinoma Symptoms

Choroid plexus carcinoma symptoms can vary, depending upon the location and size of the tumor. They can include:

  • Cerebrospinal fluid blockage causing increased pressure on the brain and enlargement of the skull
  • Enlarged fontanelles
  • Headaches
  • Lethargy and irritability
  • Nausea and vomiting
  • Problems eating or walking

Getting Diagnosed

Our team of specialists provides the most up-to-date evaluations using the latest diagnostic and imaging technology.

We work very closely with the departments of Neurosurgery, Interventional Neuroradiology, Neurology and Radiation Oncology, as well as the Normal Pressure Hydrocephalus Center and Skull Base Center to ensure an accurate diagnosis and the appropriate treatment for the best outcome.


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